MANAGEMENT OF A DELAYED PRESENTATION OF CONGENITAL KNEE DISLOCATION IN A 14 MONTH OLD CHILD WITH LARSENS SYNDROME AND PIERRE ROBIN SEQUENCE
نویسندگان
چکیده
Larsens syndrome is a rare genetic disorder characterized by multiple joint dislocations, abnormal facial features, and ligamentous laxity.Dislocation can involve Hips, knees, elbows, other joints. it was first described Larsen et al in 1950 [1]. Pierre Robin sequence another congenital birth defect That microganthia, glossoptosis cleft palate which lead to variety of functional abnormalities including feeding , breathing hearing [2,3]. Here case report a14-month-old child with who presented late joints dislocation (elbow, hips, ankle), failed management knee dislocation.
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ژورنال
عنوان ژورنال: International journal of advanced research
سال: 2021
ISSN: ['2707-7802', '2707-7810']
DOI: https://doi.org/10.21474/ijar01/13231